Angiosarcoma cutáneo idiopático

Angiosarcoma is a rare and aggressive malignant tumor of the vascular endothelial cells. Three clinical variants are recognized: idiopathic or primary cutaneous angiosarcoma (most common form), angiosarcoma associated with chronic lymphedema and post- radiotherapy angiosarcoma. It presents varia...

Descripción completa

Guardado en:
Detalles Bibliográficos
Publicado en:Revista Médica Universitaria
Autores principales: Fernández Tapia, María Jimena, Innocenti, Carolina, Marabini, Noelia, Merino, Avelina, Parra, Viviana, Suarez Módica, Florencia
Materias:
Acceso en línea:https://bdigital.uncu.edu.ar/fichas.php?idobjeto=9266
Descripción
Sumario:Angiosarcoma is a rare and aggressive malignant tumor of the vascular endothelial cells. Three clinical variants are recognized: idiopathic or primary cutaneous angiosarcoma (most common form), angiosarcoma associated with chronic lymphedema and post- radiotherapy angiosarcoma. It presents variable clinic, with multiple differential diagnosis, being essential histopathological study and immunohisto-chemistry to arrive at an accurate diagnosis. It is characterized by a high rate of local recurrence and a high metastatic potential. Surgical excision associated with regional radiotherapy is recommended treatment. Chemotherapy and radiation therapy are reserved for unresectable lesions. We present three cases of idiopathic cutaneous angiosarcoma in patients with different epidemiological characteristics, and a bibliographic review is performed.